Erdheim-Chester Disease

Erdheim–Chester disease

Maladie de Chester-Erdheim.png

Erdheim–Chester disease (also known as Erdheim–Chester syndrome or polyostotic sclerosing histiocytosis) is a rare disease characterized by the abnormal multiplication of a specific type of white…

Consensus guidelines for the diagnosis and clinical management of Erdheim-Chester disease

Figure 1
Figure 2
Erdheim-Chester disease (ECD) is a rare, non-Langerhans histiocytosis. Recent findings suggest that ECD is a clonal disorder, marked by recurrent BRAF V600E…

First-Ever FDA Approval for Erdheim-Chester Disease

Vemurafenib okayed for BRAF-positive disease